Bjarke Baisner Laursen, Ulrik Pedersen, Thomas Kjærgaard*
Abstract:
We here present a case of an 8-year old girl with an inflammatory myofibroblastic tumour of the trachea. She was initially referred due to stridor, dyspnea, and low functional status. Diagnostic work-up revealed a cauliflower-like tumour in trachea, which was initially removed endoscopically and subsequently by tracheal resection. The patient was previously diagnosed with idiopathic thrombocytopenia, which resolved spontaneously postoperatively.
Inflammatory myofibroblastic tumours also known as inflammatory pseudo tumours are very rare primary tumours of the trachea and considered by the WHO to represent intermediate grade of malignancy. Any association between this condition and idiopathic thrombocytopenia has so far only been described sporadically.
We here present a case of an 8-year old girl with an inflammatory myofibroblastic tumour of the trachea. She was initially referred due to stridor, dyspnea, and low functional status. Diagnostic work-up revealed a cauliflower-like tumour in trachea, which was initially removed endoscopically and subsequently by tracheal resection. The patient was previously diagnosed with idiopathic thrombocytopenia, which resolved spontaneously postoperatively.
Inflammatory myofibroblastic tumours also known as inflammatory pseudo tumours are very rare primary tumours of the trachea and considered by the WHO to represent intermediate grade of malignancy. Any association between this condition and idiopathic thrombocytopenia has so far only been described sporadically.
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