Julian Küstermeyer*, Helmut Ostertag, Jörg Hattingen and Hans-Jürgen Welkoborsky
Abstract:
Background: Tumors of the temporal bone in general and particular in children are extremely rare. The anatomical conditions of that special anatomic region can cause misleading symptoms. Diagnosis of rare tumor entities of the skull base in children is a challenging interdisciplinary task.
Objective: The purpose of the present article is to describe the diagnostic process of a rare pathologic condition and review the literature with current opinions of diagnostic and therapeutic methods with respect to angiosarcomas.
Methods: We report about a 13 years old boy with an angiosarcoma of the temporal bone. A review of the literature with particular emphasis on the diagnostic procedures was performed.
Results: The clinical and histological characteristics are reported in here. To date less than 20 cases of angiosarcomas of the temporal bone are published in the literature. Although a large variety of diagnostic methods is available, diagnosing and grading of such a rare tumor is still challenging.
Conclusion: Angiosarcoma of the temporal bone is extremely rare. The symptoms are unspecific, and can mimicking, like in this case, an acute mastoiditis. Diagnosis is challenging and only possible by Immunohistochemical examinations. Diagnosis of such rare pathologic conditions requires an interdisciplinary teamwork and collaboration of different institutions. Current technologies allow an easy exchange of knowledge all around the world for characterizing diseases precisely, and getting the experience of specialists together. This is crucial for a targeted and effective treatment.
Background: Tumors of the temporal bone in general and particular in children are extremely rare. The anatomical conditions of that special anatomic region can cause misleading symptoms. Diagnosis of rare tumor entities of the skull base in children is a challenging interdisciplinary task.
Objective: The purpose of the present article is to describe the diagnostic process of a rare pathologic condition and review the literature with current opinions of diagnostic and therapeutic methods with respect to angiosarcomas.
Methods: We report about a 13 years old boy with an angiosarcoma of the temporal bone. A review of the literature with particular emphasis on the diagnostic procedures was performed.
Results: The clinical and histological characteristics are reported in here. To date less than 20 cases of angiosarcomas of the temporal bone are published in the literature. Although a large variety of diagnostic methods is available, diagnosing and grading of such a rare tumor is still challenging.
Conclusion: Angiosarcoma of the temporal bone is extremely rare. The symptoms are unspecific, and can mimicking, like in this case, an acute mastoiditis. Diagnosis is challenging and only possible by Immunohistochemical examinations. Diagnosis of such rare pathologic conditions requires an interdisciplinary teamwork and collaboration of different institutions. Current technologies allow an easy exchange of knowledge all around the world for characterizing diseases precisely, and getting the experience of specialists together. This is crucial for a targeted and effective treatment.
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